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ATR

ATR serine/threonine kinase
General Information
Name ATR serine/threonine kinase
Alias
  • serine/threonine-protein kinase ATR
  • FRAP-related protein-1
  • MEC1, mitosis entry checkpoint 1, homolog
  • ataxia telangiectasia and Rad3-related protein
Gene_family Armadillo like helical domain containing
organism Homo sapiens
entrez_id 545
location 3q23
transcript_count 9
exon_count 49
Location
3p26.3p24.3p22.2p21.31p14.3p12.3q11.2q13.13q21.2q23q25.31q26.31q28
by NCBI GRCh38.p14
Summary
    Entrez The protein encoded by this gene is a serine/threonine kinase and DNA damage sensor, activating cell cycle checkpoint signaling upon DNA stress. The encoded protein can phosphorylate and activate several proteins involved in the inhibition of DNA replication and mitosis, and can promote DNA repair, recombination, and apoptosis. This protein is also important for fragile site stability and centrosome duplication. Defects in this gene are a cause of Seckel syndrome 1. [provided by RefSeq, Aug 2017]
    Stringdb Serine/threonine-protein kinase ATR; Serine/threonine protein kinase which activates checkpoint signaling upon genotoxic stresses such as ionizing radiation (IR), ultraviolet light (UV), or DNA replication stalling, thereby acting as a DNA damage sensor. Recognizes the substrate consensus sequence [ST]-Q. Phosphorylates BRCA1, CHEK1, MCM2, RAD17, RPA2, SMC1 and p53/TP53, which collectively inhibit DNA replication and mitosis and promote DNA repair, recombination and apoptosis. Phosphorylates 'Ser-139' of histone variant H2AX/H2AFX at sites of DNA damage, thereby regulating DNA damage r [...]
    nextProt Serine/threonine protein kinase which activates checkpoint signaling upon genotoxic stresses such as ionizing radiation (IR), ultraviolet light (UV), or DNA replication stalling, thereby acting as a DNA damage sensor. Recognizes the substrate consensus sequence [ST]-Q. Phosphorylates BRCA1, CHEK1, MCM2, RAD17, RPA2, SMC1 and p53/TP53, which collectively inhibit DNA replication and mitosis and promote DNA repair, recombination and apoptosis. Phosphorylates 'Ser-139' of histone variant H2AX at sites of DNA damage, thereby regulating DNA damage response mechanism. Required for FANCD2 ubiquitination. Critical for maintenance of fragile site stability and efficient regulation of centrosome duplication. Positively regulates the restart of stalled replication forks following activation by the KHDC3L-OOEP scaffold complex (By similarity).
Interactions
NCBI
StringDB
Ontologies
Pathways
Transcripts
Accession Version MolecularType Name NCBI Comments
NM_001354579 2 mRNA transcript variant 2 NC_000003 Reference
XM_011512925 2 mRNA transcript variant X4 NC_000003 Reference
NM_001184 4 mRNA transcript variant 1 NC_000003 Reference
XM_011512924 2 mRNA transcript variant X1 NC_000003 Reference
XM_047448361 1 mRNA transcript variant X3 NC_000003 Reference
XM_047448360 1 mRNA transcript variant X2 NC_000003 Reference
XM_047448363 1 mRNA transcript variant X6 NC_000003 Reference
XM_047448362 1 mRNA transcript variant X5 NC_000003 Reference
XM_047448364 1 mRNA transcript variant X7 NC_000003 Reference